Hematology and Oncology Book

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Acute Vaso-Occlusive Episode in Sickle Cell Anemia

Aka: Acute Vaso-Occlusive Episode in Sickle Cell Anemia, Sickle Cell Crisis, Vaso-Occlusive Pain Crisis, Sickle Cell Pain Crisis
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  1. See Also
    1. Sickle Cell Anemia
  2. Precipitating Factors
    1. Preceded by infection 25% of the time
      1. Human Parvovirus B19 is a common viral cause
    2. Cold Weather due to reflex vasospasm
    3. Dehydration in warm weather
  3. Symptoms
    1. Child under age 18 years
    2. Recurrent painful crises
    3. Sudden onset pain in Abdomen, chest, back and joints
  4. Labs
    1. Profound Anemia
    2. Reticulocyte Count <1%
  5. Management
    1. Pain control for acute crisis
      1. Requires aggressive Narcotic Analgesia
      2. Consider Patient Controlled Analgesia (PCA Pump)
      3. Morphine is preferred over Meperidine (Seizure risk)
    2. Intravenous fluids
      1. Avoid Fluid Overload
      2. Limit total fluid to <1.5x maintenance requirements
    3. Oxygen if Hypoxia present
    4. Incentive Spirometry
  6. Course
    1. Acute Crisis usually resolves spontaneously 7-10 days
  7. References
    1. Preboth (2000) Am Fam Physician 61

Hemoglobin SS disease with crisis (C0238425)

Definition (CSP) broad term used to describe several different acute conditions occurring with sickle cell disease, including aplastic crisis, hemolytic crisis, and vasoocclusive crisis.
Concepts Disease or Syndrome (T047)
ICD9 282.62
ICD10 D57.0, D57.00
SnomedCT 417425009, 72279006, 191197002
English SICKLE CELL CRISIS, Hemoglobin S disease with crisis, Sickle-cell anaemia with crisis, Sickle-cell anemia with crisis, Haemoglobin S disease with crisis, Sickle cell anaemia with crisis, SIckle cell anaemia with crisis, sickle cell crisis (diagnosis), sickle cell crisis, anemia hemolytic sickle Hb-SS disease with crisis, anemia hemolytic sickle cell crisis, sickle cell-hemoglobin SS disease with crisis, sickle cell-hemoglobin SS disease with crisis (diagnosis), Sickle cell anaem with crisis, HB-S disease with mention of crisis, Hb-SS disease with crisis, Hb-SS disease w crisis, Sickle-cell disease NOS with crisis, Hb-SS disease with crisis, unspecified, sickle cell anemia crisis, cell crisis sickle, crisis disease hb-s mention, sickle-cell crisis, anemia cell crisis sickle, cells crisis sickle, crisis; sickle-cell, disease (or disorder); sickle-cell, with crisis, sickle-cell; anemia, with crisis, sickle-cell; crisis, sickle-cell; disorder, with crisis, anemia; sickle-cell, with crisis, Hb-S disease with mention of crisis, Sickle-cell crisis NOS, Sickle cell crisis, Sickle cell anemia with crisis, Hemoglobin S disease with crisis (disorder), Sickle cell anemia with crisis (disorder), Haemoglobin SS disease with crisis, Hemoglobin SS disease with crisis, Hemoglobin SS disease with crisis (disorder)
Italian Anemia a cellule falciformi con crisi, Emoglobinopatia -S con menzione di crisi, Emoglobinopatia SS con crisi, Crisi falciforme
Dutch Hb-SS aandoening met crisis, HB-S aandoening met vermelding van crisis, sikkelcelanemiecrisis, aandoening; sikkelcel, met crisis, anemie; sikkelcel, met crisis, crisis; sikkelcel, sikkelcel; aandoening, met crisis, sikkelcel; anemie, met crisis, sikkelcel; crisis, Sikkelcelanemie met crisis, sikkelcelanemie met crisis
French Hémoglobine S avec mention de crise, Hémoglobine SS avec crise drépanocytaire, Drépanocytose avec crise, Crise drépanocytaire
German HB-SS-Krankheit mit Krise, Sichelzellerkrise, HB-S-Krankheit mit Erwaehnung einer Krise, Sichelzellenanaemie mit Krisen, Sichelzellanaemie mit Krise
Portuguese Anemia de células falciformes com crises, Doença Hb-SS com crises, Doença Hb-S com referência a crises, Crise de células falciformes, Anemia de células falciformes com crise
Spanish Crisis de anemia falciforme, Enfermedad de la Hb SS con crisis, Enfermedad de la Hb S con mención de crisis, Anemia drepanocítica con crisis, drepanocitosis con crisis hemolítica (trastorno), anemia de células falciformes con crisis, anemia de células falciformes con crisis (trastorno), enfermedad por hemoglobina S con crisis, drepanocitosis con crisis, Anemia de células falciformes con crisis, enfermedad por hemoglobina SS con crisis hemolítica (trastorno), enfermedad por hemoglobina SS con crisis hemolítica
Japanese ヘモグロビンＳ症クリーゼ, 鎌状赤血球貧血クリーゼ, ヘモグロビンＳＳ疾患クリーゼ, 鎌状赤血球クリーゼ, ﾚﾝｼﾞｮｳｾｯｹｯｷｭｳﾋﾝｹﾂｸﾘｰｾﾞ, ﾍﾓｸﾞﾛﾋﾞﾝSSｼｯｶﾝｸﾘｰｾﾞ, ｶﾏｼﾞｮｳｾｯｹｯｷｭｳﾋﾝｹﾂｸﾘｰｾﾞ, ﾍﾓｸﾞﾛﾋﾞﾝSｼｮｳｸﾘｰｾﾞ, ﾚﾝｼﾞｮｳｾｯｹｯｷｭｳｸﾘｰｾﾞ
Czech Krize u srpkovité anémie, Homozygotní forma srpkovité anémie s vasookluzivní krizí, Hemoglobinopatie S s uvedením krize, Srpkovitá anémie s krizí
Korean 발증을 동반한 낫적혈구 빈혈
Hungarian Hb-Ss betegség crisissel, Sarlóssejtes anaemia crisissel, Sarlós sejt crisis, Sarlós sejt anaemia crisissel, Hb-S betegség crisis említésével
Sources
Derived from the NIH UMLS (Unified Medical Language System)


Sickle cell pain crisis (C0546176)

Concepts Finding (T033)
English Pain crisis due to sickle cell anemia, Sickle cell pain crisis, SICKLE CELL PAIN CRISIS, sickle cell pain crisis, cell crisis pain sickle, sickle cell crisis pain
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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