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AutoimmunityAka: Autoimmune Conditions

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  1. Epidemiology
    1. Women account for 75% of autoimmunity
    2. Age of onset is most common in young adult women
  2. Mechanism
    1. Autoantibody, T-Cell mediated self tissue destruction
    2. Predisposing factors
      1. Autoimmunity increases with age: lower self tolerance
      2. Genetic predisposition
    3. Protective factors
      1. Autoimmunity less common where high antigen exposure
      2. Protective exposures in first year of life
        1. Eating dirt
        2. Living on a farm
        3. House pet
        4. Day care
      3. References
        1. Weiss (2002) N Engl J Med 347:930
  3. Dermatologic Autoimmune Conditions
    1. Psoriasis
    2. Dermatitis herpeteformis
    3. Pemphigus Vulgaris
    4. Vitiligo
    5. Alopecia Areata
  4. Endocrine Autoimmune Conditions
    1. Insulin Dependent Diabetes Mellitus
    2. Grave's Disease
    3. Hashimoto's Thyroiditis
    4. Addison's Disease
  5. Gastrointestinal Autoimmune Conditions
    1. Crohn's Disease
    2. Ulcerative Colitis
    3. Primary Biliary Cirrhosis
    4. Autoimmune Hepatitis
  6. Hematologic Autoimmune Conditions
    1. Autoimmune Hemolytic Anemia
    2. Pernicious Anemia
    3. Autoimmune Thrombocytopenia
  7. Musculoskeletal Autoimmune Conditions
    1. Rheumatoid Arthritis
    2. Systemic Lupus Erythematosus
    3. Scleroderma
    4. Polymyositis
    5. Dermatomyositis
    6. Sjogren's Syndrome
    7. Ankylosing Spondylitis
  8. Neurologic Autoimmune Conditions
    1. Multiple Sclerosis
    2. Myasthenia Gravis
    3. Guillain-Barre Syndrome
  9. Vascular Autoimmune Conditions
    1. Temporal Arteritis
    2. Anti-phospholipid Syndrome
    3. Wegener's Granulomatosis
    4. Behcet's Syndrome
  10. References
    1. Zuber (2003) AAFP Board Review, Seattle

Autoimmunity (C0004368)

Definition (MSH)Process whereby the immune system reacts against the body's own tissues. Autoimmunity may produce or be caused by AUTOIMMUNE DISEASES.
Definition (CSP)developmentally complex, not necessarily pathological, possibly pervasive, cell or humoral immune system reactivity toward autologous (self) antigens; do not confuse with AUTOIMMUNE DISORDER.
Definition (NCI)Autoimmune Status; the state of a person's health in regard to autoimmune disease or antibody presence.
ConceptsPathologic Function (T046)
MSHD015551
EnglishAutoimmune state, Autoimmune Status, Autoimmunities, Autoimmunity
Spanishautoinmunidad, estado autoinmune
Parent ConceptsImmunity (C0020964), Health Status (C0018759), Immune system finding (C1291764)
SourcesCSP, MSH, NCI, SCTSPA, SNOMEDCT
Derived from the NIH UMLS (Unified Medical Language System)



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