Neonatology Book

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Bronchopulmonary Dysplasia

Aka: Bronchopulmonary Dysplasia
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  1. Definition
    1. Chronic Lung Disease in Infants and Children
    2. Occurs secondary to Hyaline Membrane Disease associated with Prematurity
  2. Epidemiology
    1. Incidence increases with earlier gestational ages
    2. Incidence increases with lower birth weights
      1. Incidence: Affects 50-80% of infants with birth weight <900 grams
  3. Management
    1. See Pediatric Asthma
    2. Home oxygen may be required
    3. Car Seats may need adjustment (restraint may exacerbate symptoms)
      1. Require Car Seat test before NICU discharge
      2. Special prone or supine car safety device may be indicated
  4. Complications
    1. Respiratory infections
      1. Increased susceptibility
      2. Increased severity
    2. Reactive Airways
      1. Episodic respiratory distress and Wheezing
    3. Growth Delay
      1. Require higher caloric intakes due to increased work of breathing
  5. Course
    1. Lung function often normalizes by teen years

Bronchopulmonary Dysplasia (C0006287)

Definition (MSH) A chronic lung disease developed after OXYGEN INHALATION THERAPY or mechanical ventilation (VENTILATION, MECHANICAL) usually occurring in certain premature infants (INFANT, PREMATURE) or newborn infants with respiratory distress syndrome (RESPIRATORY DISTRESS SYNDROME, NEWBORN). Histologically, it is characterized by the unusual abnormalities of the bronchioles, such as METAPLASIA, decrease in alveolar number, and formation of CYSTS.
Definition (NCI) A non-neoplastic lung disorder which develops in premature neonates who have been treated with oxygen and mechanical ventilation.
Definition (CSP) chronic lung disease of infants, possibly related to oxygen toxicity or barotrauma, characterized by bronchiolar metaplasia and interstitial fibrosis.
Concepts Disease or Syndrome (T047)
MSH D001997
ICD10 P27.8
SnomedCT 67569000
English Bronchopulmonary Dysplasia, Dysplasia, Bronchopulmonary, BRONCHOPULMONARY DYSPLASIA, bronchopulmonary dysplasia, BPD - Bronchopulmon dysplasia, Chron lung disease of prematur, Perinatal bronchopulm.dysplas., BRONCHOPULM DYSPLASIA, BPD, bronchopulmonary dysplasia of fetus or newborn, bronchopulmonary dysplasia of fetus or newborn (diagnosis), Bronchopulmonary Dysplasia [Disease/Finding], bronchopulmonary dysplasia (BPD), chronic lung disease of babies, Bronchopulmonary dysplasia of newborn, BPD - Bronchopulmonary dysplasia, Bronchopulmonary dysplasia, Chronic lung disease of prematurity, Perinatal bronchopulmonary dysplasia, Ventilator lung in newborn, Bronchopulmonary dysplasia of newborn (disorder), bronchopulmonary; dysplasia, dysplasia; bronchopulmonary, ventilator lung; newborn
Dutch chronische longziekte t.g.v. vroeggeboorte, bronchopulmonaal; dysplasie, dysplasie; bronchopulmonaal, ventilator lung; pasgeborene, bronchopulmonaire dysplasie, Bronchopulmonale dysplasie, Dysplasie, bronchopulmonale
French Maladie pulmonaire chronique de la prématurité, Dysplasie bronchopulmonaire, Dysplasie broncho-pulmonaire
German chronische Lungenerkrankung bei Fruehgeburt, bronchopulmonale Dysplasie, Bronchopulmonale Dysplasie
Italian Pneumopatia cronica del prematuro, Displasia broncopolmonare
Portuguese Doença crónica dos pulmões de prematuridade, Displasia broncopulmonar, Displasia Broncopulmonar
Spanish Enfermedad pulmonar crónica del prematuro, displasia broncopulmonar del recién nacido (trastorno), displasia broncopulmonar del recién nacido, displasia broncopulmonar, Displasia broncopulmonar, Displasia Broncopulmonar
Japanese 未熟児慢性肺疾患, 気管支肺異形成症, キカンシハイイケイセイショウ, ミジュクジマンセイハイシッカン
Swedish Bronkopulmonell dysplasi
Czech bronchopulmonální dysplazie, Bronchopulmonální dysplazie, Předčasná chronická plicní choroba
Finnish Bronkopulmonaalinen dysplasia
Russian BRONKHOLEGOCHNAIA DISPLAZIIA, БРОНХОЛЕГОЧНАЯ ДИСПЛАЗИЯ
Polish BPD, Dysplazja oskrzelowo-płucna
Hungarian Bronchopulmonalis dysplasia, Éretlen tüdő chronikus betegsége
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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