Otolaryngology Book

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Otosclerosis

Aka: Otosclerosis
  1. Definition
    1. Ankylosis between stapes footplate and surrounding bone of the inner ear
  2. Epidemiology
    1. Most often presents in middle-aged white women
    2. Gender predominance: Twice as common in women
    3. Family History is present in 50% of cases
      1. Autosomal dominant trait, with poor penetrance
  3. Pathophysiology
    1. Abnormal bone deposition at base of stapes (footplate)
    2. Stapes fixed to oval window and unable to vibrate
  4. Signs
    1. Conductive Hearing Loss or mixed Hearing Loss
    2. Hearing Loss usually limited to 50 decibels
    3. Disproportionately effects low frequencies most commonly
    4. Bilateral involvement is most common
  5. Management
    1. Hearing Aid
    2. Sodium fluoride: halts or retards progression
    3. Surgery: Stapedotomy or Stapedectomy
      1. Restore transmission with middle ear prosthesis
      2. Improvement in 95% of patients

Otosclerosis (C0029899)

Definition (CSP) pathological condition of the bony labyrinth of the ear, in which there is formation of spongy bone; may cause bony ankylosis of the stapes, resulting in conductive hearing loss; cochlear otosclerosis may also develop, resulting in sensorineural hearing loss.
Definition (MSH) Formation of spongy bone in the labyrinth capsule which can progress toward the STAPES (stapedial fixation) or anteriorly toward the COCHLEA leading to conductive, sensorineural, or mixed HEARING LOSS. Several genes are associated with familial otosclerosis with varied clinical signs.
Concepts Disease or Syndrome (T047)
MSH D010040
ICD9 387.9, 387
ICD10 H80, H80.9, H80.90
SnomedCT 155241009, 194383003, 11543004
English Otoscleroses, Otosclerosis, Otospongioses, Otospongiosis, OTOSCLEROSIS, Otosclerosis, NOS, Otospongiosis, NOS, Otosclerosis NOS, Otosclerosis, unspecified, OTSC1, Otosclerosis syndrome, Otospongiosis syndrome, OTS, otosclerosis (diagnosis), otosclerosis, OTOSCLEROSIS, ASSOCIATION WITH, Otosclerosis NOS (disorder), Unspecified otosclerosis, Unspecified otosclerosis, unspecified ear, Otosclerosis [Disease/Finding], otoscleroses, otosclerose, OTOSCLEROSIS 1, Otosclerosis (disorder), otospongiosis
Portuguese OTOSCLEROSE, Otosclerose NE, Otoesclerose, Otosclerose, Otospongiose
Spanish OTOSCLEROSIS, Otosclerosis no especificada, Otosclerosis, Otoesclerosis, otoesclerosis (trastorno), otoesclerosis, SAI (trastorno), otoesclerosis, SAI, otoesclerosis, otoespongiosis, Otospongiosis
German OTOSKLEROSE, Otosklerose, unspezifisch, Otosklerose, nicht naeher bezeichnet, Otosklerose, Otospongiose
Dutch niet-gespecificeerde otosclerose, otospongiose, Otosclerose, niet gespecificeerd, otosclerose, Otosclerose, Otospongiose
French Otosclérose, non précisée, OTOSCLEROSE, Otosclerose, Otosclérose, Otospongiose
Italian Otosclerosi, non specificata, Otospongiosi, Otosclerosi
Japanese 詳細不明の耳硬化症, ｼｮｳｻｲﾌﾒｲﾉｼﾞｺｳｶｼｮｳ, ﾐﾐｺｳｶｼｮｳ, ｼﾞｺｳｶｼｮｳ, ｼｮｳｻｲﾌﾒｲﾉﾐﾐｺｳｶｼｮｳ, 耳硬化症, 耳硬化
Swedish Otoskleros, OTOSKLEROS
Czech otoskleróza, Otoskleróza, blíže neurčená, Otospongióza, Otoskleróza
Finnish Otoskleroosi, OTOSKLEROOSI
Russian OTODISTROFIIA, OTOSKLEROZ, OTOSPONGIOZ, ОТОДИСТРОФИЯ, ОТОСКЛЕРОЗ, ОТОСПОНГИОЗ
Norwegian OTOSKLEROSE
Danish Otosklerose
Hungarian otosclerosis, Otosclerosis, otosclerosis, nem meghatározott, Otospongiosis
Korean 상세불명의 귀경화증, 귀경화증
Croatian OTOSKLEROZA
Basque OTOSKLEROSIA
Polish Otoskleroza
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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