Dermatology Book

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Pemphigus Foliaceus

Aka: Pemphigus Foliaceus, Superficial Pemphigus, Pemphigus erythematosus, Senear-Usher Syndrome, Fogo selvagem, Pemphigus herpetiformis
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  1. See Also
    1. Bullous Disease
    2. Pemphigus
    3. Pemphigus Vulgaris
  2. Definition
    1. Less common, milder and superficial form of Pemphigus
  3. Signs
    1. Onset on skin of face in butterfly distribution
    2. May also involve scalp, chest or upper back
    3. Rarely involves Oral Mucosa
    4. Nikolsky's Sign absent
  4. Variants
    1. Pemphigus erythematosus (Senear-Usher Syndrome)
      1. Localized variant of Pemphigus Foliaceus
      2. Associated with Systemic Lupus Erythematosus
      3. Antinuclear Antibody positive
    2. Fogo selvagem
      1. Variant of Pemphigus Foliaceus
      2. Endemic to Brasil and Colombia
      3. Associated with chronic black fly exposure
    3. Pemphigus herpetiformis
      1. Pruritic Blister formation
      2. May appear similar to Dermatitis Herpetiformis
    4. Drug-Induced Pemphigus
      1. Associated with Penicillamine and Captopril
      2. Differentiate from Drug-Triggered Pemphigus
        1. Unmasks Pemphigus Vulgaris
  5. Labs: Histology
    1. Blister forms just below Stratum Corneum of Epidermis
  6. References
    1. Habif (1996) Clinical Dermatology, Mosby, p. 510
    2. Cotell (2000) Am J Emerg Med 18(3):288-99

Pemphigus and fogo selvagem (C0263314)

Concepts Disease or Syndrome (T047)
MSH C535551
ICD10 L10.3
SnomedCT 200906007, 46459009
English Brazilian pemphigus, Brazilian pemphigus [fogo selvagem], Brazilian pemphigus foliaceus (diagnosis), fogo selvagem, Brazilian pemphigus (disorder), Endemic pemphigus foliaceus, Pemphigus and fogo selvagem, South American pemphigus, wild fire, Amendola's syndrome, Brazilian pemphigus foliaceus, Fogo selvagem, Wildfire pemphigus, Wild fire, Brazilian pemphigus foliaceus (disorder), Brazilian; pemphigus, pemphigus; Brazilian
Spanish Brazilian pemphigus, fuego salvaje, pénfigo foliáceo brasilero, pénfigo foliáceo brasileño (trastorno), pénfigo foliáceo brasileño, síndrome de Améndola
German Brasilianischer Pemphigus [fogo selvagem]
Korean 브라질 천포창[포고 셀바젬병]
Dutch Braziliaans; pemphigus, pemphigus; Braziliaans, Braziliaanse pemphigus [fogo selvagem]
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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