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Autoimmune Pancreatitis
- Epidemiology
- Uncommon cause of Chronic Pancreatitis
- Average age: 63 years (More than 80% are over age 50 years)
- Male gender predominance by 2 fold
- Symptoms: Presentations
- Jaundice (>60%)
- Abdominal Pain (>30%)
- Associated Conditions
- Sjogren's Syndrome
- Rheumatoid Arthritis
- Inflammatory Bowel Disease
- Diagnosis
- IgG4 titer
- Significantly increased in autoimmune Pancreatitis
- CT abdomen
- Diffuse pancreatitic involvement
- Management
- Prednisone 40 mg/day for 1 week and then taper dose down by 5 mg weekly
- References
- Finkelberg (2006) N Engl J Med 355:2670
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