II. Pathophysiology

  1. Not infectious
  2. Rare collagen vascular disease
  3. Affects at least 2 cartilaginous sites

III. Symptoms and signs

  1. Auricle
    1. Pain and swelling
    2. Inflammation and local destruction
  2. Ear lobe is spared
  3. Sensorineural Hearing Loss may be associated
  4. Vertigo in 20% of cases

IV. Diagnosis

  1. Biopsy

V. Management

  1. Systemic Corticosteroids
  2. Refer to Otolaryngology (ENT)

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Ontology: Polychondritis, Relapsing (C0032453)

Definition (MSH) An acquired disease of unknown etiology, chronic course, and tendency to recur. It is characterized by inflammation and degeneration of cartilage and can result in deformities such as floppy ear and saddle nose. Loss of cartilage in the respiratory tract can lead to respiratory obstruction.
Concepts Disease or Syndrome (T047)
MSH D011081
ICD10 M94.1
SnomedCT 111256009, 85780006, 72275000
English Polychondritides, Relapsing, Relapsing Polychondritides, Relapsing Polychondritis, Polychondritis, Chronic Atrophic, Atrophic Polychondritides, Chronic, Atrophic Polychondritis, Chronic, Chronic Atrophic Polychondritides, Chronic Atrophic Polychondritis, Polychondritides, Chronic Atrophic, RELAPSING POLYCHONDRITIS, relapsing polychondritis (diagnosis), relapsing polychondritis, Polychondritis, Relapsing, Polychondritis, Relapsing [Disease/Finding], polychondritis relapsing, chronic polychondritis, Systemic chondromalacia (disorder), Relapsing polychondritis, Chronic polychondritis, Systemic chondromalacia, Meyenburg's disease, Relapsing polychondritis (disorder), polychondritis; recrudescent [Brill-Zinsser], recrudescent [Brill-Zinsser]; polychondritis, Systemic chondromalacia -RETIRED-, Chondromalacia, systemic, Chronic atrophic polychondritis
Spanish policondritis recidivante, policondritis recidivante (trastorno), Policondritis atrófica crónica, Policondritis recidivante, policondritis crónica, policondritis crónica (trastorno), condromalacia sistémica - RETIRADO -, condromalacia sistémica - RETIRADO - (concepto no activo), condromalacia sistémica, Policondritis Atrófica Crónica, Policondritis Recurrente
Dutch recidiverende polychondritis, chronische atrofische polychondritis, polychondritis; recidiverend, recidiverend; polychondritis, Polychondritis, chronische atrofische, Polychondritis, recidiverende, Recidiverende polychondritis
German chronische atrophische Polychondritis, rezivierende Polychondritis, Panchondritis [Rezidivierende Polychondritis], Polychondritis chronica atrophicans, Polychondritis, rezidivierende
Italian Policondrite atrofica cronica, Policondrite cronica atrofica, Policondrite recidivante
Portuguese Policondrite recorrente, Policondrite atrófica crónica, Policondrite Atrófica Crônica, Policondrite Recidivante
Swedish Återfallspolykondrit
Japanese マンセイイシュクセイタハツセイナンコツエン, サイハツセイタハツセイナンコツエン, 軟骨炎-再発性多発性, 再発性多発性軟骨炎, 慢性萎縮性多発性軟骨炎, 多発性軟骨炎-再発性, 軟骨炎-慢性萎縮性多発性
Finnish Uusiutuva monirustotulehdus
Russian POLIKHONDRIT RETSIDIVIRUIUSHCHII, ПОЛИХОНДРИТ РЕЦИДИВИРУЮЩИЙ
Czech Relabující polychondritida, Chronická atrofická polychondritida, relapsující polychondritida, recidivující polychondritida, relabující polychondritida, polychondritida recidivující
Korean 재발성 다발연골염
Polish Zapalenie chrząstek nawracające, Zapalenie wielochrząstne nawracające, Zapalenie chrząstek zanikowe
Hungarian Krónikus atrophiás polychondritis, Recurrens polychondritis
Norwegian Polychondritis chronica atrophicans, Residiverende polykondritt
French Polychondrite chronique atrophiante, Polychondrite récidivante, Polychondrite à rechute