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Rhabdomyolysis
- Definition
- Skeletal muscle breakdown
- Pathophysiology
- Muscle injury allows calcium influx
- Increased intracellular calcium destroys muscle fibers
- Release of muscle fiber contents into circulation
- Myoglobin
- Potassium
- Phosphate
- Creatine Phosphokinase
- Uric Acid
- Myoglobin overloads Haptoglobin binding capacity
- Myoglobin blocks renal tubules
- Results in Renal Failure
- Causes
- Signs
- Muscle pain (myalgias)
- Muscle Weakness
- Localized swelling or bruising
- Constitutional symptoms
- Urinary tract symptoms
- Tea-colored urine
- Anuria
- Labs
- Urinalysis: Findings suggestive of Myoglobinuria
- Dipstick orthotoluidine positive for blood
- No Red Blood Cells seen in freshly spun sediment
- Creatine Phosphokinase increased
- CPK over 16,000 associated with Renal Failure
- Myoglobin level increased in urine or serum
- Results not available for days after sending sample
- Not helpful in acute diagnosis
- Urinalysis: Findings suggestive of Myoglobinuria
- Complications
- Electrolyte disturbance
- Acute Renal Failure (Acute Tubular Necrosis)
- Accounts for 5 to 15% of Acute Renal Failure cases
- Mechanism: Myoglobin overload, hypovolemia, acidosis
- Associated with Creatinine kinase over 16,000 units/L
- Miscellaneous complications
- Liver inflammation
- Cardiac arrhythmia or Cardiac Arrest
- Disseminated Intravascular Coagulation
- Compartment Syndrome
- Management: Intravenous fluids
- Initial: Forced diuresis
- Start immediately (especially in first 6 hours)
- Protocol
- Normal Saline 1.5 Liters per hour
- Urine output should approach 300 ml/hour
- End-points
- No Myoglobinuria
- Creatine Phosphokinase (CPK) less than 1000
- Maintenance: Alkalinize Urine pH > 6.5
- Protocol
- Saline 0.45% with
- Sodium Bicarbonate 40 meq (1 to 2 ampules) and
- Mannitol 10 grams per liter
- Contraindications
- Persistent oliguria despite hydration listed above
- Hypocalcemia (provoked by Sodium Bicarbonate)
- Protocol
- Monitoring of elderly with comorbid conditions
- Intensive care unit admission
- Hourly vital signs including input and output
- Consider invasive monitoring
- Initial: Forced diuresis
- Management: Acute Renal Failure
- Results from Acute Tubular Necrosis
- Daily Hemodialysis may be indicated
- Many patients show partial or complete renal recovery
- Precautions
- Aggressive hydration is critical
- Avoid Diuretics (may provoke Renal Failure)
- Do not correct Hypocalcemia unless symptomatic
- Anticipate Serum Calcium increase in recovery phase
- Calcium re-mobilized from injured muscles
- References
- Marx in Rosen (2002) Emergency Medicine 1762-70
- Sauret (2002) Am Fam Physician 65(5):907
Rhabdomyolysis (C0035410) | |
|---|---|
| Definition (MSH) | Necrosis or disintegration of skeletal muscle often followed by myoglobinuria. |
| Concepts | Pathologic Function (T046) |
| ICD9 | 728.88 |
| MSH | D012206 |
| English | Rhabdomyolyses, Rhabdomyolysis |
| Spanish | rabdomiolisis |
| Parent Concepts | Myopathy (C0026848), MYOSITIC DISORDERS (C0549655), Other muscle, ligament and fascia disorder (C0158361), Lysis (C0024348), Degenerative disorder (C1285162), Disorder of skeletal muscle (C1533847) |
| Sources | AOD, COSTAR, CST, ICD9CM, MSH, NDFRT, OMIM, SCTSPA, SNOMEDCT Derived from the NIH UMLS (Unified Medical Language System) |