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Horner's Syndrome

Aka: Horner's Syndrome
  1. Pathophysiology
    1. Paralysis of superior cervical Sympathetic Nerve
      1. Destructive lesion to superior cervical Ganglion
      2. Destruction in posterior retroparotid space
      3. Mediastinal tumor
    2. Associated lesions
      1. Cranial Nerve 9
      2. Cranial Nerve 10
      3. Cranial Nerve 11
      4. Cranial Nerve 12
  2. Causes
    1. Brainstem stroke
    2. Posterior retroparotid space mass
      1. Parotid Gland tumor
      2. Carotid body tumor
      3. Metastatic tumor
      4. Lymphoma
      5. Tuberculous Adenitis
    3. Mediastinal mass
  3. Signs
    1. Mnemonic: Miosis, Ptosis, Anhydrosis
    2. All findings are unilateral
    3. Miosis
    4. Palpebral Ptosis (Incomplete)
      1. Contrast with complete Ptosis in levator paralysis
      2. Illusion of eyeball recession (No true enophthalmos)
    5. Absence of sweating (Anhydrosis) on face and neck

Ocular-Ophthalmoplegia, Sympathetic (C0019937)

Definition (NCI) A condition in which one side of the face is flushed, does not produce sweat, and has a constricted pupil and drooping eyelid. It can be caused by an injury to, or paralysis of, nerves in the neck, or by a tumor.
Definition (MSH) A syndrome associated with defective sympathetic innervation to one side of the face, including the eye. Clinical features include MIOSIS; mild BLEPHAROPTOSIS; and hemifacial ANHIDROSIS (decreased sweating)(see HYPOHIDROSIS). Lesions of the BRAIN STEM; cervical SPINAL CORD; first thoracic nerve root; apex of the LUNG; CAROTID ARTERY; CAVERNOUS SINUS; and apex of the ORBIT may cause this condition. (From Miller et al., Clinical Neuro-Ophthalmology, 4th ed, pp500-11)
Definition (CSP) syndrome associated with defective sympathetic innervation to one side of the face, including the eye; clinical features include miosis, mild blepharoptosis, and hemifacial anhidrosis (decreased sweating); lesions of the brain stem, cervical spinal cord, first thoracic nerve root, apex of the lung, carotid artery, cavernous sinus, and apex of the orbit may cause this condition.
Concepts Disease or Syndrome (T047)
MSH D006732
ICD10 G90.2
SnomedCT 12731000, 192915005, 192922002
English Bernard's syndrome, Cervical sympathetic syndrome, Oculosympathetic syndrome, Bernard Syndrome, Bernard's Syndrome, Bernards Syndrome, Horner Syndrome, Horner's Syndrome, Horners Syndrome, Syndrome, Bernard's, Syndrome, Horner's, CERVICAL SYMPATHETIC PARALYSIS SYNDROME, CLAUDE BERNARD-HORNER SYNDROME, HORNER SYNDROME, OPHTHALMOPLEGIA, SYMPATHETIC, Syndrome, Claude Bernard-Horner, Horner syndrome, HORNER'S SYNDROME, Bernard Horner syndrome, Horner's syndrome (diagnosis), cervical sympathetic paralysis, cervical sympathetic paralysis (diagnosis), Ocular-Ophthalmoplegia, Sympathetic, Claude Bernard Horner Syndrome, Claude Bernard-Horner Syndrome, Syndrome, Bernard, Syndrome, Horner, Ocular Ophthalmoplegia, Sympathetic, Ophthalmoplegia, Sympathetic Ocular, Sympathetic Ocular Ophthalmoplegia, Sympathetic Ocular-Ophthalmoplegia, Ocular Ophthalmoplegias, Sympathetic, Ocular-Ophthalmoplegias, Sympathetic, Ophthalmoplegias, Sympathetic Ocular, Sympathetic Ocular Ophthalmoplegias, Sympathetic Ocular-Ophthalmoplegias, Oculosympathetic Syndrome, Oculosympathetic Syndromes, Syndrome, Oculosympathetic, Syndromes, Oculosympathetic, Bernard(-Horner) syndrome, Horner Syndrome [Disease/Finding], claude bernard-horner syndrome, sympathetic ophthalmoplegia, bernard horner syndrome, horner's syndrome, horners syndrome, horner syndrome, Bernard Syndromes, Syndromes, Bernard, Horner's syndrome, Cervical sympathetic paralysis, Cervical sympathetic paralysis (disorder), Horner, cervical; paralysis, sympathetic (syndrome), cervical; sympathetic paralysis (syndrome), cervical; syndrome, sympathetic paralysis, Bernard-Horner, paralysis; cervical sympathetic, paralysis; sympathetic, cervical, Claude Bernard-Horner, sympathetic; cervical paralysis (syndrome), sympathetic; paralysis, cervical (syndrome), sympathetic; paralysis, cervical, sympathetic; syndrome, cervical paralysis, syndrome; cervical, sympathetic paralysis, syndrome; sympathetic, cervical paralysis
Portuguese SINDROME DE HORNER, Paralisia Óculo-Simpática, Síndrome de Bernard, Síndrome de Horner, Síndrome Óculo-Simpática Paralítica, Síndrome Óculo-Simpática
Swedish Horners syndrome
Spanish mielopatía por parálisis de nervios simpáticos, Horner syndrome, Horner's syndrome, síndrome de Horner, mielopatía por parálisis de nervios simpáticos (trastorno), parálisis simpática cervical, parálisis simpática cervical (trastorno), Sindrome de Horner, Parálisis Óculosimpática, Síndrome de Bernard, Síndrome de Horner, Síndrome de Parálisis Simpáticocervical, Síndrome Oculosimpático Paralítico, Síndrome Oculosimpático, Paralisis Oculosimpatica, Sindrome Oculosimpatico Paralitico, Sindrome Oculosimpatico, Sindrome de Bernard, Sindrome de Paralisis Simpaticocervical
Japanese ホルネルショウコウグン, ベルナール・ホルネル症候群, ベルナール症候群, ホルネル症候群, 神経支配欠損性縮瞳, ホルナー症候群, 眼交感神経系症候群, Bernard-Horner症候群, 縮瞳-神経支配欠損性, Bernard症候群, Horner症候群
Czech Hornerův syndrom
Finnish Hornerin oireyhtymä
Russian GORNERA SINDROM, BERNARA-GORNERA SINDROM, БЕРНАРА-ГОРНЕРА СИНДРОМ, ГОРНЕРА СИНДРОМ
German HORNER SYNDROM, Horner Syndrom, Bernard-Syndrom, Horner-Syndrom, Horner-Bernard-Syndrom, Okulopupilläres Syndrom
French SYNDROME DE HORNER, Syndrome de Horner, Syndrome oculaire sympathique, Syndrome de Claude Bernard-Horner, SCBH, Syndrome oculo-sympathique, Syndrome oculosympathique, Syndrome sympathique cervical
Italian Sindrome oculo-simpatica, Sindrome oculosimpatica, Sindrome di Claude Bernard-Horner, Oftalmoplegia oculare, Sindrome di Horner
Korean 호르너 증후군
Polish Zespół Hornera
Hungarian Horner-syndroma
Dutch cervicaal; paralyse, sympathicus (syndroom), cervicaal; sympathicusparalyse (syndroom), cervicaal; syndroom, sympathicusparalyse, paralyse; cervicaal sympathisch, paralyse; sympathisch, cervicaal, sympathicus; cervicale paralyse (syndroom), sympathicus; paralyse, cervicaal (syndroom), sympathicus; syndroom, cervicale paralyse, sympathisch; paralyse, cervicaal, syndroom; cervicaal, sympathische paralyse, syndroom; sympathicus, cervicale paralyse, syndroom van Horner, Bernard-syndroom, Horner-syndroom, Oculosympathisch syndroom, Syndroom van Horner, Syndroom, Horner-
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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