Hematology and Oncology Book

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Myelofibrosis

Aka: Myelofibrosis
  1. Pathophysiology
    1. Normal Bone Marrow replaced by fibrotic material
  2. Symptoms and Signs
    1. Weight loss
    2. Excessive Bleeding from skin and mucous membranes
  3. Diagnosis
    1. Bone Marrow Biopsy: Dry tap

Myelofibrosis (C0026987)

Definition (NCI) A partial or complete replacement of the bone marrow stroma by fibrous tissue. It can be a primary bone marrow lesion as part of the chronic myeloproliferative disorders (chronic idiopathic myelofibrosis), a manifestation of acute myeloid leukemia (acute panmyelosis with myelofibrosis), or a secondary phenomenon due to bone marrow involvement by a metastatic tumor (e.g., metastatic breast carcinoma). --2003
Definition (CSP) replacement of the bone marrow by fibrous tissue, occurring in association with a myeloproliferative disorder or secondary to another unrelated condition.
Definition (NCI) A disorder in which the bone marrow is replaced by fibrous tissue.
Concepts Neoplastic Process (T191)
MSH D009191
ICD9 289.83
ICD10 D75.81
SnomedCT 78956007, 52967002, 154841009, 267572005
English Myelofibrosis, Agnogenic myeloid metaplasia, MYELOFIBROSIS, Myelofibrosis, NOS, Myelosclerosis, NOS, Myelosis-non-leukemic, myelofibrosis, myelofibrosis (diagnosis), Myelosclerosis (disorder), Myelosis non-leukaemic, Myelosis-non-leukaemic, Myelosis non-leukemic, Myelosis nonleukemic, Myelofibrosis NOS, chronic idiopathic myelofibrosis, myelofibrose, fibrosis bone marrow, bone fibrosis marrow, bone marrow fibrosis, mos, Myelosclerosis, MF - Myelofibrosis, Myelofibrosis (disorder), myelosclerosis, Bone Marrow Fibrosis
French MYELOFIBROSE, Myélose non leucémique, Myélofibrose
Portuguese MIELOFIBROSE, Mielose não leucémica, Mielofibrose
Spanish MIELOFIBROSIS, Mielosis no leucémica, Myelofibrosis, esclerosis de la médula ósea, fibrosis de la médula ósea, mielofibrosis (trastorno), mielofibrosis, mielosclerosis (concepto no activo), mielosclerosis, Mielofibrosis
German MYELOFIBROSE, Myelose nicht-leukaemisch, Myelofibrose
Italian Mielofibrosi, Mielosi non leucemica
Dutch myelosis niet-leukemisch, myelosis-niet-leukaemisch, myelosis niet-leukaemisch, myelofibrosis
Japanese 骨髄線維症, コツズイセンイショウ, 非白血病性骨髄症, ヒハッケツビョウセイコツズイショウ
Finnish Myelofibroosi
Czech Neleukemická myelóza, Myelofibróza
Hungarian Nem leukaemiás myelosis, Nem-leukaemiás myelosis, Myelofibrosis, Nem leukemiás myelosis, Nem-leukemiás myelosis
Sources
Derived from the NIH UMLS (Unified Medical Language System)


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