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Myelofibrosis
Aka: Myelofibrosis- Pathophysiology
- Normal Bone Marrow replaced by fibrotic material
- Symptoms and Signs
- Weight loss
- Excessive Bleeding from skin and mucous membranes
- Diagnosis
- Bone Marrow Biopsy: Dry tap
Myelofibrosis (C0026987) |
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| Definition (NCI) | A partial or complete replacement of the bone marrow stroma by fibrous tissue. It can be a primary bone marrow lesion as part of the chronic myeloproliferative disorders (chronic idiopathic myelofibrosis), a manifestation of acute myeloid leukemia (acute panmyelosis with myelofibrosis), or a secondary phenomenon due to bone marrow involvement by a metastatic tumor (e.g., metastatic breast carcinoma). --2003 |
| Definition (CSP) | replacement of the bone marrow by fibrous tissue, occurring in association with a myeloproliferative disorder or secondary to another unrelated condition. |
| Definition (NCI) | A disorder in which the bone marrow is replaced by fibrous tissue. |
| Concepts | Neoplastic Process (T191) |
| MSH | D009191 |
| ICD9 | 289.83 |
| ICD10 | D75.81 |
| SnomedCT | 78956007, 52967002, 154841009, 267572005 |
| English | Myelofibrosis, Agnogenic myeloid metaplasia, MYELOFIBROSIS, Myelofibrosis, NOS, Myelosclerosis, NOS, Myelosis-non-leukemic, myelofibrosis, myelofibrosis (diagnosis), Myelosclerosis (disorder), Myelosis non-leukaemic, Myelosis-non-leukaemic, Myelosis non-leukemic, Myelosis nonleukemic, Myelofibrosis NOS, chronic idiopathic myelofibrosis, myelofibrose, fibrosis bone marrow, bone fibrosis marrow, bone marrow fibrosis, mos, Myelosclerosis, MF - Myelofibrosis, Myelofibrosis (disorder), myelosclerosis, Bone Marrow Fibrosis |
| French | MYELOFIBROSE, Myélose non leucémique, Myélofibrose |
| Portuguese | MIELOFIBROSE, Mielose não leucémica, Mielofibrose |
| Spanish | MIELOFIBROSIS, Mielosis no leucémica, Myelofibrosis, esclerosis de la médula ósea, fibrosis de la médula ósea, mielofibrosis (trastorno), mielofibrosis, mielosclerosis (concepto no activo), mielosclerosis, Mielofibrosis |
| German | MYELOFIBROSE, Myelose nicht-leukaemisch, Myelofibrose |
| Italian | Mielofibrosi, Mielosi non leucemica |
| Dutch | myelosis niet-leukemisch, myelosis-niet-leukaemisch, myelosis niet-leukaemisch, myelofibrosis |
| Japanese | 骨髄線維症, コツズイセンイショウ, 非白血病性骨髄症, ヒハッケツビョウセイコツズイショウ |
| Finnish | Myelofibroosi |
| Czech | Neleukemická myelóza, Myelofibróza |
| Hungarian | Nem leukaemiás myelosis, Nem-leukaemiás myelosis, Myelofibrosis, Nem leukemiás myelosis, Nem-leukemiás myelosis |
| Sources |
Derived from the NIH UMLS (Unified Medical Language System) |