Hematology and Oncology Book

Coagulopathy

Platelet Disorders

http://www.fpnotebook.com/

Osler-Rendu-Weber DiseaseAka: Hereditary Hemorrhagic Telangiectasia

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  1. Pathophysiology
    1. Autosomal dominant inheritance
    2. Profuse Telangiectasias form throughout the body
      1. Number of lesions increases with age
  2. Symptoms
    1. Profuse hemorrhages
    2. Frequent Epistaxis
  3. Signs
    1. Bright red elevated telangiectasias
      1. Blanch with pressure
  4. Labs
    1. Coagulation Factors Normal
    2. Complete Blood Count
      1. May show Anemia

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