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Klippel-Trenaunay-Weber Syndrome
Aka: Klippel-Trenaunay-Weber Syndrome, Parkes-Weber Syndrome- Signs
- Port-Wine Stain over an extremity
- Extremity soft tissue and bony hypertrophy
- Evaluation
- Measure length and girth of extremity every 3-6 month
- If extremity elongation noted:
- Evaluate for arteriovenous fistula
- Evaluate for venous atresia