Dermatology Book

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Klippel-Trenaunay-Weber SyndromeAka: Parkes-Weber Syndrome

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  1. Signs
    1. Port-Wine Stain over an extremity
    2. Extremity soft tissue and bony hypertrophy
  2. Evaluation
    1. Measure length and girth of extremity every 3-6 month
    2. If extremity elongation noted:
      1. Evaluate for arteriovenous fistula
      2. Evaluate for venous atresia

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