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Congenital Melanocytic NevusAka: Congenital Melanocytic Nevi, Garment Nevi, Giant Congenital Nevi

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  1. Epidemiology
    1. Prevalence: Up to 2% of newborns
  2. Pathophysiology
    1. Neural crest Melanocytes and their precursors with disrupted migration
  3. Signs
    1. Brown to black lesions that are typically flat (but can be elevated)
  4. Complications: Melanoma
    1. Large lesions may develop Melanoma in up to 0.7% of cases
    2. Giant congenital nevi >20 cm (adult size) carry up to a 6% lifetime risk of Melanoma
    3. Small congenital nevi <1.5 cm (adult size) rarely progress to Melanoma
  5. Management
    1. Large congenital melanocytic nevi
      1. Criteria
        1. Garment nevi or giant congenital nevi: >14 cm in infants (>20 cm in adults)
        2. Large congenital nevi: >12 cm head or >7 cm elsewhere in infants (>20 cm adults)
      2. Protocol
        1. Excise lesion
        2. Close observation for recurrence (excision does not eliminate risk completely)
    2. Medium congenital melanocytic nevi
      1. Criteria: 0.5 to 7 cm in infants (1.5 to 20 cm in adults)
      2. Protocol: Close observation by dermatology
    3. Small congenital melanocytic nevi
      1. Criteria: <0.5 cm in infants (<1.5 cm in adults)
      2. Protocol: Close observation by primary provider
  6. References
    1. Berg (2003) {a 2411} Res 13:441
    2. Krengel (2006) Br J Dermatol 155:1
    3. McLaughlin (2008) Am Fam Physician 77:56

Congenital melanocytic nevus (C1318558)

ConceptsCongenital Abnormality (T019) , Neoplastic Process (T191)
EnglishCongenital dermal melanocytic naevus, Congenital dermal melanocytic nevus, Congenital melanocytic naevus, Congenital melanocytic naevus of skin, Congenital melanocytic nevus, Congenital melanocytic nevus of skin, Congenital Melanocytic Nevus of the Skin, Congenital Nevus of Skin, Congenital Nevus of the Skin, Congenital pigmented melanocytic naevus, Congenital pigmented melanocytic naevus of skin, Congenital pigmented melanocytic nevus, Congenital pigmented melanocytic nevus of skin, Congenital pigmented naevus, Congenital pigmented naevus of skin, Congenital pigmented nevus, Congenital pigmented nevus of skin, Congenital Pigmented Nevus of the Skin, Congenital Pigmented Skin Nevus, Congenital Skin Nevus
Spanishnevo congenito melanocitico pigmentado, nevo congenito pigmentado melanocitico de piel, nevo melanocitico congenito, nevus congenito pigmentado melanocitico de piel, nevus melanocitico congenito
Parent ConceptsMelanocytic nevus (C0027962), Melanocytic tumor of skin (C0349501), Hamartoma (C0018552), Ambiguous concept (C1274012), Congenital hamartoma (C1302749), Congenital hamartoma of skin (C1302821), Melanocytic nevus - category (C1302831), Congenital melanocytic nevus (C1318558), Duplicate concept (C1274013)
SourcesMTH, NCI, SCTSPA, SNOMEDCT
Derived from the NIH UMLS (Unified Medical Language System)



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